[Case of cardiac amyloidosis associated with IgG-K multiple myeloma in the framework of restrictive myocardiopathy]

Cardiologia. 1999 Feb;44(2):193-7.
[Article in Italian]

Abstract

Primary amyloidosis, due to amassing of fragments of light chains of IgG, often causes cardiac involvement. We describe a 65-year-old woman with multiple myeloma efficaciously treated with chemotherapy. Amyloidosis had been supported by myelic biopsy. The patient came to our observation because of right heart failure, hypotension and syncope: she was treated with a dopamine i.v. and was in cachectic status. She had a moderate pericardial effusion. ECG showed reduction of QRS amplitude, I degree atrioventricular block, posterior fascicular and right bundle branch block. Right cardiac catheterization showed a restrictive situation. After 1 week exitus occurred by asystole. In this case, there were other involvements by amyloidosis, besides the cardia one: that of autonomic nervous system and, probably, surrenal.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Aged
  • Amyloidosis / complications*
  • Amyloidosis / pathology
  • Biopsy
  • Bone Marrow / pathology
  • Cardiomyopathy, Restrictive / complications*
  • Cardiomyopathy, Restrictive / diagnosis
  • Electrocardiography
  • Female
  • Humans
  • Immunoglobulin G*
  • Immunoglobulin kappa-Chains*
  • Multiple Myeloma / complications*
  • Multiple Myeloma / immunology

Substances

  • Immunoglobulin G
  • Immunoglobulin kappa-Chains