Severe hepatitis and pure red cell aplasia in adult Still's disease: good response to immunosuppressive therapy

Dig Dis Sci. 1999 Aug;44(8):1639-42. doi: 10.1023/a:1026631514623.

Abstract

Adult-onset Still's disease is a systemic inflammatory disorder with a highly variable clinical course. Mild hepatitis and anemia are common manifestations. We describe a patient with adult Still's disease who developed a severe hepatitis and a life-threatening pure red cell aplasia. The hepatitis developed after treatment with NSAIDs was started. The patient was successfully treated with a combination of prednisone, cyclosporin, and methotrexate. Physicians should be aware that severe hepatitis and pure red cell aplasia can occur in adult Still's disease. We recommend a careful monitoring of liver functions in patients with adult Still's disease who are being treated with NSAIDs.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Anti-Inflammatory Agents / therapeutic use
  • Cyclosporine / therapeutic use
  • Female
  • Hepatitis / etiology*
  • Hepatitis / pathology
  • Hepatitis / physiopathology
  • Humans
  • Immunosuppression Therapy*
  • Immunosuppressive Agents / therapeutic use
  • Methotrexate / therapeutic use
  • Prednisone / therapeutic use
  • Red-Cell Aplasia, Pure / etiology*
  • Red-Cell Aplasia, Pure / pathology
  • Still's Disease, Adult-Onset / complications*
  • Still's Disease, Adult-Onset / therapy*

Substances

  • Anti-Inflammatory Agents
  • Immunosuppressive Agents
  • Cyclosporine
  • Prednisone
  • Methotrexate