Treatment with a gonadotropin-releasing-hormone analog and attainment of full height potential in a male monozygotic twin with gonadotropin-releasing hormone-dependent precocious puberty

Eur J Pediatr. 1999 Nov;158(11):933-5. doi: 10.1007/s004310051245.

Abstract

We report on a pair of male monozygotic twins, one unaffected and the other affected with gonadotropin-releasing hormone (GnRH)-dependent precocious puberty, and discuss the role of treatment with a GnRH analog in the attainment of full height potential in GnRH-dependent precocious puberty. At 1.6 years of age, the affected twin was studied for tall stature (+3.8 SD), and was diagnosed as having GnRH-dependent precocious puberty due to a hypothalamic hamartoma of the tuber cinereum. He was treated with oral cyproterone acetate (110-170 mg/m(2) daily) from 1.8 through 5. 0 years of age, with oral cyproterone acetate and intranasal buserelin acetate (700-900 microg/m(2) daily) from 5.0 through 7.5 years, and with intranasal buserelin acetate alone (1100- 1400 microg/m(2) daily) from 7.5 through 12.6 years. He attained a final height of 171.0 cm at 14.9 years of age (+0.10 SD) and his twin 170. 0 cm at 15.3 years of age (-0.10 SD), with their target height being 174.5 +/- 9.0 cm.

Conclusion: This study indicates that GnRH analog treatment may preserve near full height potential in some patients with GnRH-dependent precocious puberty.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Administration, Inhalation
  • Administration, Oral
  • Body Height / drug effects
  • Buserelin / administration & dosage*
  • Child, Preschool
  • Cyproterone Acetate / administration & dosage*
  • Drug Therapy, Combination
  • Follow-Up Studies
  • Gonadotropin-Releasing Hormone / biosynthesis
  • Growth Disorders / diagnosis
  • Growth Disorders / drug therapy*
  • Growth Disorders / etiology
  • Hamartoma / complications
  • Hamartoma / diagnosis
  • Humans
  • Hypothalamic Diseases / complications
  • Hypothalamic Diseases / diagnosis
  • Magnetic Resonance Imaging
  • Male
  • Progesterone Congeners / administration & dosage*
  • Puberty, Precocious / complications
  • Puberty, Precocious / diagnosis
  • Puberty, Precocious / drug therapy*
  • Treatment Outcome
  • Twins, Monozygotic

Substances

  • Progesterone Congeners
  • Gonadotropin-Releasing Hormone
  • Cyproterone Acetate
  • Buserelin