Introduction: Eccrine sweat gland carcinoma, which belongs to the eccrine sweat gland carcinoma family, is a rare malignancy of the skin with a potential aggressive growth and metastatic spread.
Exegesis: We report here a case of malignant eccrine poroma arising on the upper leg, with widespread pulmonary metastases.
Conclusion: A brief synopsis of the pathological and clinical aspects of eccrine sweat gland carcinoma is presented with the currently available therapies.