Oblique facial clefts are said to account for 0.25% of all clefts. Craniosynostosis is not known to be associated with oblique facial clefting, although craniofrontonasal dysplasia is well described. Craniosynostosis and oblique facial clefting presenting together in the same patient is a rare event. We present such a case, and detail the treatment plan to allow simultaneous correction of both deformities.