Muellerian aplasia associated with ring chromosome 8p12q12 mosaicism

Am J Med Genet A. 2003 Jan 30;116A(3):290-4. doi: 10.1002/ajmg.a.10902.

Abstract

We report on a woman with Muellerian aplasia, renal and skeletal anomalies, and minor dysmorphic signs. Conventional cytogenetic analysis revealed mosaicism for a small supernumerary, undefinable ring chromosome. Chromosome microdissection and reverse painting demonstrated that this marker contained pericentric material from chromosome 8 (8p12q12). Thus, we identified a Muellerian aplasia phenotype with partial trisomy 8 mosaicism.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adolescent
  • Chromosome Banding
  • Chromosomes, Human, Pair 8 / genetics*
  • Female
  • Humans
  • In Situ Hybridization, Fluorescence
  • Karyotyping
  • Mosaicism / genetics*
  • Mullerian Ducts / abnormalities*
  • Ring Chromosomes*
  • Uterus / abnormalities
  • Vagina / abnormalities