Refractory anemia with excess of blasts in transformation: analysis of reclassification according to the WHO proposals

Leuk Res. 2003 May;27(5):397-404. doi: 10.1016/s0145-2126(02)00220-5.

Abstract

The category of "refractory anemia with excess blasts in transformation" (RAEB-T) has been abandoned in the new WHO-classification of myelodysplastic syndromes (MDS). The majority of patients previously belonging to this category are now classified as acute myeloid leukaemia (AML). In the FAB-classification, patients had been assigned to the RAEB-T category if they had either (1) a medullary blast count between 20 and 30% or (2) a peripheral blast count of at least 5%, or (3) Auer rods detectable, irrespective of the blast count. We analyzed these subtypes of RAEB-T in terms of hematological characteristics, karyotype anomalies, and prognosis. Patients with more than 20% medullary blasts and patients with at least 5% peripheral blasts as the sole defining parameter for RAEB-T had a median survival of 6 months, as compared to 11 months in patients with Auer rods as the sole defining parameter. The presence of Auer rods therefore does not convey a particularly bad prognosis and does not justify placing patients in a high-risk category of MDS or even classifying them as AML. This finding supports the elimination of Auer rods as a parameter for classification in the new WHO system. On the other hand, the reclassification into RAEB II (according to WHO proposals) of previous RAEB-T patients with a peripheral blast count of at least 5% is problematic, because this feature predicts a median survival not different from that of AML patients.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acute Disease
  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Anemia, Refractory, with Excess of Blasts / blood
  • Anemia, Refractory, with Excess of Blasts / classification*
  • Anemia, Refractory, with Excess of Blasts / mortality
  • Anemia, Refractory, with Excess of Blasts / pathology
  • Blood Cell Count
  • Cell Transformation, Neoplastic
  • Female
  • Humans
  • Inclusion Bodies / ultrastructure
  • Karyotyping
  • L-Lactate Dehydrogenase / blood
  • Leukemia, Myeloid / blood
  • Leukemia, Myeloid / classification*
  • Leukemia, Myeloid / mortality
  • Leukemia, Myeloid / pathology
  • Life Tables
  • Male
  • Middle Aged
  • Myelodysplastic Syndromes / classification*
  • Neoplasm Proteins / blood
  • Neoplastic Stem Cells / pathology
  • Prognosis
  • Risk
  • Survival Analysis
  • World Health Organization

Substances

  • Neoplasm Proteins
  • L-Lactate Dehydrogenase