Reversible acute axonal polyneuropathy associated with Wernicke-Korsakoff syndrome: impaired physiological nerve conduction due to thiamine deficiency?

J Neurol Neurosurg Psychiatry. 2003 May;74(5):674-6. doi: 10.1136/jnnp.74.5.674.

Abstract

Acute axonal polyneuropathy and Wernicke-Korsakoff encephalopathy developed simultaneously in three patients. Nerve conduction studies (NCS) detected markedly decreased compound muscle action potentials (CMAPs) and sensory nerve action potentials (SNAPs) with minimal conduction slowing; sympathetic skin responses (SSRs) were also notably decreased. Sural nerve biopsies showed only mild axonal degeneration with scattered myelin ovoid formation. The symptoms of neuropathy lessened within two weeks after an intravenous thiamine infusion. CMAPs, SNAPs, and SSRs also increased considerably. We suggest that this is a new type of peripheral nerve impairment: physiological conduction failure with minimal conduction delay due to thiamine deficiency.

Publication types

  • Case Reports

MeSH terms

  • Acute Disease
  • Adult
  • Axons / drug effects
  • Axons / physiology*
  • Humans
  • Korsakoff Syndrome / drug therapy
  • Korsakoff Syndrome / etiology*
  • Korsakoff Syndrome / physiopathology*
  • Male
  • Middle Aged
  • Neural Conduction / drug effects
  • Neural Conduction / physiology*
  • Polyneuropathies / drug therapy
  • Polyneuropathies / etiology*
  • Polyneuropathies / physiopathology*
  • Thiamine / therapeutic use
  • Thiamine Deficiency / complications*
  • Thiamine Deficiency / drug therapy
  • Thiamine Deficiency / physiopathology*

Substances

  • Thiamine