[Alpha]B-crystallin genotype has impact on the multiple sclerosis phenotype

Neurology. 2003 Nov 11;61(9):1245-9. doi: 10.1212/01.wnl.0000091861.27246.9e.

Abstract

Background: Both multiple sclerosis (MS) susceptibility and MS clinical phenotype are in part genetically determined. [Alpha]B-crystallin is a candidate autoantigen in MS, and there are three polymorphisms in the promoter region of the encoding gene (CRYAB): at positions -C249G, -C650G, and -A652G.

Methods: These polymorphisms were studied in sporadic cases of MS, assessing disease susceptibility, clinical phenotype, and MRI appearance.

Results: The CRYAB polymorphisms influenced susceptibility as well as disease expression in MS.

Conclusion: Carriers of the rare allele CRYAB-650*C had an increased likelihood of a noninflammatory, neurodegenerative phenotype characterized by a relatively rapid, primary progressive clinical disease course.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Brain / pathology
  • Female
  • Gene Frequency
  • Genetic Predisposition to Disease
  • Genotype
  • Humans
  • Linear Models
  • Linkage Disequilibrium
  • Longitudinal Studies
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Multiple Sclerosis / diagnosis*
  • Multiple Sclerosis / epidemiology
  • Multiple Sclerosis / genetics*
  • Netherlands / epidemiology
  • Odds Ratio
  • Phenotype
  • Polymorphism, Genetic / genetics
  • Severity of Illness Index
  • alpha-Crystallin B Chain / genetics*

Substances

  • alpha-Crystallin B Chain