Nasal gliomas are tumors of extracranial neuroglial tissue. The incidence is very low, with little more than 300 cases described unliterature. It is important to make a correct diagnosis study of this lesion, to avoid the possible complications derived from an erroneous treatment. We review a case of one girl with midline nasal tumor, she was operated on with total extirpation of the tumor, we analyze the previous diagnosis study and their histopathology.