Effectiveness and safety of combined iron-chelation therapy with deferoxamine and deferiprone

Hematol J. 2004;5(6):475-9. doi: 10.1038/sj.thj.6200550.

Abstract

Introduction: The purpose of our study was to evaluate the effectiveness and safety of combined therapy with deferoxamine (DFO) and deferiprone (DFP) in patients with beta-thalassemia major and increased serum ferritin.

Patients and methods: Our study was performed in 36 patients with beta-thalassemia major. DFP was administered orally in a total daily dose of 60 mg/kg for 6 days per week and DFO was administered subcutaneously in a total daily dose of 40-50 mg/kg for 4-6 days per week. The efficacy of combined treatment was assessed by measurements of serum ferritin and 24-h urine iron excretion levels.

Results: Out of the 36 patients, 11 discontinued DFO after a mean of 4 months; however, 25 patients, who continued to receive the combined therapy showed a very satisfactory compliance. After a mean of 13.5 months, their mean serum ferritin levels reduced from 2637 + 1292 to 1580 + 1024 ng/ml (P = 0.002) and their mean urinary iron excretion elevated from 0.41 + 0.27 to 0.76 +0.49 mg/24h (P = 0.003). The observed side effects were gastrointestinal disorders,elevations in liver enzymes, mild neutropenia, joint symptoms, taste disorders, dizziness and fatigue.

Conclusions: The results of this study show that combined iron-chelation therapy with DFO and DFP results in satisfactory reduction of serum ferritin with no significant toxicity.

Publication types

  • Clinical Trial

MeSH terms

  • Administration, Oral
  • Adolescent
  • Adult
  • Deferiprone
  • Deferoxamine / administration & dosage*
  • Deferoxamine / adverse effects
  • Dose-Response Relationship, Drug
  • Drug Administration Schedule
  • Drug Therapy, Combination
  • Female
  • Ferritins / blood
  • Ferritins / drug effects
  • Humans
  • Injections, Subcutaneous
  • Iron / urine
  • Iron Chelating Agents / administration & dosage*
  • Iron Chelating Agents / adverse effects
  • Male
  • Middle Aged
  • Pyridones / administration & dosage*
  • Pyridones / adverse effects
  • Treatment Outcome
  • beta-Thalassemia / drug therapy*

Substances

  • Iron Chelating Agents
  • Pyridones
  • Deferiprone
  • Ferritins
  • Iron
  • Deferoxamine