Peripheral obliterating arterial disease characterized by aortoiliac steno-occlusion occurring in relatively young women of small stature, is frequently reported in the literature under the name small aorta syndrome. Although it remains unclear whether small aorta syndrome represents a separate entity, the small size of the distal aorta increases risk for aortoiliac occlusive disease. Patients usually present with lower extremity claudication and typical risk factors. This paper shows an analysis of the literature focusing on the pathogenesis, clinical features, risk factors and treatment, as well as a single center experience with this disorder.