Coronary aneurysm formation and subsequent stenosis resulting in ischemic heart disease are the most important complications of Kawasaki disease (KD). Reported is the evolution of severe calcific coronary artery stenosis in an 8-year-old boy managed with percutaneous transluminal coronary rotational ablation (PTCRA) after failed balloon angioplasty. No restenosis occurred 6 months after RA. Reports on PTCRA in children are limited and it may be a good therapeutic option as a definite or a palliative one to postpone coronary artery bypass surgery in the young children with calcific coronary artery stenosis after Kawasaki disease.