Many patients with ventriculoarterial discordance have survived to adulthood. Those with complete transposition of the great arteries have often had an atrial switch procedure (Mustard or Senning operation) performed, which leaves the morphological right ventricle supporting the systemic circulation. It has been also reported previously undiagnosed congenitally corrected transposition of the great arteries. We present the complete transposition of the great arteries in an 8-year-old Romanian child with a septal defect of the ventricle (functionally single ventricle).