Pheochromocytoma is a rare disease, which often presents a diagnostic challenge due to a variable symptom presentation complex. We report the case of a child who presented with isolated symptoms of palpitations and was found to have junctional tachycardia with subsequent development of cardiomyopathy. Further evaluation revealed that she had an extra-adrenal pheochromocytoma, which was the cause of her arrhythmia and subsequent symptomatology.