The cuprizone model for demyelination

Acta Neurol Scand Suppl. 2008:188:72-6. doi: 10.1111/j.1600-0404.2008.01036.x.

Abstract

Background: Important advances in multiple sclerosis (MS) research have been made as a direct or indirect result of experiments in animal models for the disease, although MS is a disease only affecting humans. The cuprizone model is a model for toxic demyelination. In this model, young mice are fed with the copper chelator cuprizone, leading to oligodendrocyte death and a subsequent reversible demyelination. Spontaneous remyelination can be seen as early as 4 days after withdrawal of cuprizone.

Materials and methods: This article reviews previous research on this model and discusses the potential of the model for future application in MS research.

Discussion: The cuprizone model correlates with newer histopathological data in MS and is a valuable tool for studies on de- and remyelination. The use of the C57BL/6 strain offers the potential for future studies on transgene and knockout mice.

Publication types

  • Review

MeSH terms

  • Animals
  • Chelating Agents*
  • Cuprizone*
  • Disease Models, Animal*
  • Mice
  • Multiple Sclerosis / chemically induced*
  • Multiple Sclerosis / pathology*
  • Myelin Sheath / drug effects

Substances

  • Chelating Agents
  • Cuprizone