A case showing the typical clinical and pathological features of splenic micronodular T-cell/histiocyte-rich large B-cell lymphoma is presented. Since the series recorded by Dogan et al (Am J Surg Pathol 2003;27:903-911), there have been very few reports on this lymphoma variant. Our case presents minor variations on the recorded features. Possible reasons for the scarcity of reports and for the confirmation of this lymphoma as a variant of T-cell-rich large B-cell lymphoma are discussed.