IIlizarov external fixator for bilateral severe flexion deformity of the knee in haemophilia: case report

Arch Orthop Trauma Surg. 2010 May;130(5):621-5. doi: 10.1007/s00402-009-0968-8. Epub 2009 Sep 16.

Abstract

Introduction: Deformity correction by Illizarov method in haemophilic patients is a rare phenomenon.

Aim: To correct the bilateral knee deformity by Illizarov in one sitting.

Materials and methods: Patient had fixed flexion deformity (100 degrees ) of both knees; posterior skin webs, posterior subluxation, wasting of quadriceps and <1% level of factor IX. Patient was managed with optimisation of factor IX level in perioperative period by factor IX supplementations. Deformities were corrected by Illizarov's fixator on both lower limbs at 3 months and fixator was removed at 4 months. At 3 months, patient developed bilateral equinus deformity which was corrected by a dynamic foot sling and gentle tendoachillis stretching exercises.

Result: Patient had superficial pin tract infection at three sites. There were no episodes of bleeding from pin tracts or in knee joint during distraction period. Patient had bilateral knees flexion up to 120 degrees with 5 degrees extensor lag on the right side. Patient is going to college and walks with intermittent use of a hinge knee brace at 3 years follow-up.

Conclusion: Illizarov method is a safe, less invasive, effective, economical and truly biological method for correction of severe flexion deformities of knee in haemophilic patients.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Braces
  • External Fixators*
  • Factor IX / administration & dosage
  • Hemophilia B / complications*
  • Humans
  • Joint Deformities, Acquired / etiology
  • Joint Deformities, Acquired / surgery*
  • Knee Joint*
  • Male

Substances

  • Factor IX