Introduction: The amniotic band syndrome has a scarce prevalence and intrauterine death as a result of amniotic bands formation is extremely rare.
Case presentation: We present an illustrative case of intrauterine death of an embryo in the 24th gestational week in an 30-year old primigravida. The death was ascribed to the twisting of the umbilical cord around the left upper extremity, causing a strangulation of the umbilical cord in a very impressive way.
Conclusion: Constriction of the umbilical cord by an amniotic band is extremely rare and very hard, if not impossible, to diagnose with antenatal sonography.