Both normal memory counts and decreased naive cells favor intrinsic defect over early senescence of Down syndrome T lymphocytes

Pediatr Res. 2010 May;67(5):557-62. doi: 10.1203/PDR.0b013e3181d4eca3.

Abstract

Because of their increased malignancies, autoimmune diseases, and infections, patients with Down syndrome (DS) show features of immunodeficiency. The DS thymus and T lymphocyte subsets have indeed proven to be different, and this has been interpreted as precocious aging. Our study on T lymphocyte subpopulations in DS shows that the normal expansion of naive helper (CD4CD45RA) and cytotoxic (CD8CD45RACD27) T lymphocytes is lacking in the first years of life; this is more logically explainable with an intrinsic T lymphocyte defect. Furthermore, memory cell numbers are not different from age-matched controls (AMC), which does not support the hypothesis of precocious aging. Although the absolute numbers of T lymphocyte subpopulations approach AMC levels toward adulthood, the persistent clinical problems suggest that these cells may not function optimally. However, the clinical picture does not fit severe T lymphocyte deficiency. The latter concept is also supported by our finding that cytomegalovirus (CMV)-seropositive DS children show similar numbers of terminally differentiated cytotoxic T lymphocytes when compared with healthy children, not increased numbers as are seen in immunocompromised hosts.

MeSH terms

  • Adolescent
  • Antibodies, Viral / blood
  • CD4-Positive T-Lymphocytes / immunology*
  • CD4-Positive T-Lymphocytes / virology
  • CD8-Positive T-Lymphocytes / immunology*
  • CD8-Positive T-Lymphocytes / virology
  • Cellular Senescence*
  • Child
  • Child, Preschool
  • Cytomegalovirus / immunology
  • Down Syndrome / immunology*
  • Female
  • Humans
  • Immunologic Deficiency Syndromes / immunology*
  • Immunologic Memory*
  • Immunophenotyping
  • Infant
  • Lymphocyte Count
  • Male
  • Retrospective Studies
  • T-Lymphocyte Subsets / immunology*
  • T-Lymphocyte Subsets / virology
  • Young Adult

Substances

  • Antibodies, Viral