Competing interactions stabilize pro- and anti-aggregant conformations of human Tau

J Biol Chem. 2011 Jun 10;286(23):20512-24. doi: 10.1074/jbc.M111.237875. Epub 2011 Apr 15.

Abstract

Aggregation of Tau into amyloid-like fibrils is a key process in neurodegenerative diseases such as Alzheimer. To understand how natively disordered Tau stabilizes conformations that favor pathological aggregation, we applied single-molecule force spectroscopy. Intramolecular interactions that fold polypeptide stretches of ~19 and ~42 amino acids in the functionally important repeat domain of full-length human Tau (hTau40) support aggregation. In contrast, the unstructured N terminus randomly folds long polypeptide stretches >100 amino acids that prevent aggregation. The pro-aggregant mutant hTau40ΔK280 observed in frontotemporal dementia favored the folding of short polypeptide stretches and suppressed the folding of long ones. This trend was reversed in the anti-aggregant mutant hTau40ΔK280/PP. The aggregation inducer heparin introduced strong interactions in hTau40 and hTau40ΔK280 that stabilized aggregation-prone conformations. We show that the conformation and aggregation of Tau are regulated through a complex balance of different intra- and intermolecular interactions.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Alzheimer Disease / genetics
  • Alzheimer Disease / metabolism
  • Frontotemporal Dementia / genetics
  • Frontotemporal Dementia / metabolism
  • Humans
  • Mutation
  • Protein Folding*
  • Protein Structure, Quaternary
  • Protein Structure, Tertiary
  • tau Proteins / chemistry*
  • tau Proteins / genetics
  • tau Proteins / metabolism

Substances

  • MAPT protein, human
  • tau Proteins