Anti-ceramide antibody prevents the radiation gastrointestinal syndrome in mice

J Clin Invest. 2012 May;122(5):1786-90. doi: 10.1172/JCI59920. Epub 2012 Apr 2.

Abstract

Radiation gastrointestinal (GI) syndrome is a major lethal toxicity that may occur after a radiation/nuclear incident. Currently, there are no prophylactic countermeasures against radiation GI syndrome lethality for first responders, military personnel, or remediation workers entering a contaminated area. The pathophysiology of this syndrome requires depletion of stem cell clonogens (SCCs) within the crypts of Lieberkühn, which are a subset of cells necessary for postinjury regeneration of gut epithelium. Recent evidence indicates that SCC depletion is not exclusively a result of DNA damage but is critically coupled to ceramide-induced endothelial cell apoptosis within the mucosal microvascular network. Here we show that ceramide generated on the surface of endothelium coalesces to form ceramide-rich platforms that transmit an apoptotic signal. Moreover, we report the generation of 2A2, an anti-ceramide monoclonal antibody that binds to ceramide to prevent platform formation on the surface of irradiated endothelial cells of the murine GI tract. Consequently, we found that 2A2 protected against endothelial apoptosis in the small intestinal lamina propria and facilitated recovery of crypt SCCs, preventing the death of mice from radiation GI syndrome after high radiation doses. As such, we suggest that 2A2 represents a prototype of a new class of anti-ceramide therapeutics and an effective countermeasure against radiation GI syndrome mortality.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antibodies, Monoclonal, Murine-Derived / pharmacology*
  • Antibodies, Monoclonal, Murine-Derived / therapeutic use
  • Antibodies, Neutralizing / pharmacology*
  • Antibodies, Neutralizing / therapeutic use
  • Aorta / cytology
  • Apoptosis / radiation effects
  • Cattle
  • Cells, Cultured
  • Ceramides / antagonists & inhibitors*
  • Ceramides / immunology
  • Ceramides / metabolism
  • Drug Evaluation, Preclinical
  • Endothelial Cells / enzymology
  • Endothelial Cells / metabolism
  • Endothelial Cells / radiation effects
  • Enzyme Induction / radiation effects
  • Gastrointestinal Diseases / pathology
  • Gastrointestinal Diseases / prevention & control*
  • Humans
  • Intestinal Mucosa / drug effects
  • Intestinal Mucosa / pathology
  • Intestinal Mucosa / radiation effects
  • Membrane Microdomains / metabolism
  • Membrane Microdomains / radiation effects
  • Mice
  • Mice, Inbred BALB C
  • Mice, Inbred C57BL
  • Radiation Injuries, Experimental / pathology
  • Radiation Injuries, Experimental / prevention & control*
  • Sphingomyelin Phosphodiesterase / metabolism

Substances

  • Antibodies, Monoclonal, Murine-Derived
  • Antibodies, Neutralizing
  • Ceramides
  • Sphingomyelin Phosphodiesterase