Resection of adrenocortical carcinoma liver metastasis: is it justified?

Ann Surg Oncol. 2012 Aug;19(8):2643-51. doi: 10.1245/s10434-012-2358-7. Epub 2012 Apr 21.

Abstract

Background: Adrenocortical carcinoma (ACC) liver metastases (LM) represent a therapeutic challenge, and it is unclear whether resection is justified. This study assesses long-term outcome and prognostic factors after liver resection for metastatic ACC.

Methods: Patients who underwent resection of ACC LM were identified from institutional databases. Recurrence, survival, and tumor characteristics, including β-catenin and TP53 status based on immunohistochemistry and sequencing, were reviewed. The prognostic value of variables was assessed with log-rank test for univariate analysis and Cox proportional hazard models for multivariate analysis.

Results: From 1978 to 2009, 28 patients (20 females; median age, 45 years), including 11 with synchronous metastasis and 3 with extrahepatic metastasis, underwent resection for ACC LM (major hepatectomy in 61%). Postoperative mortality was nil and morbidity 55%. On pathological examination, tumors were multiple in 68%, with a median size of 43 mm, and resections were R0, 1, and 2 in 59%, 33%, and 7%, respectively. All 28 patients developed recurrent disease, which was treated surgically in 11, including repeat hepatectomy in 4. Of the 15 patients with adequate tissue for analysis, β-catenin immunostaining was positive in 7, with 4 corresponding CTNNB1 mutations associated with decreased survival; p53 staining was positive in 5 (4 with corresponding TP53 mutations). The median disease-free and overall survival after hepatectomy was 7 and 31.5 months, respectively, with a 5-year survival of 39%. In multivariate analysis, nonfunctional tumor and surgical treatment of recurrence were independent predictors of good outcome.

Conclusions: In selected patients with ACC LM, resection is associated with long-term survival and is, therefore, justified but rarely curative.

MeSH terms

  • Adrenal Cortex Neoplasms / mortality
  • Adrenal Cortex Neoplasms / pathology
  • Adrenal Cortex Neoplasms / surgery*
  • Adrenocortical Carcinoma / mortality
  • Adrenocortical Carcinoma / pathology
  • Adrenocortical Carcinoma / surgery*
  • Adult
  • Biomarkers, Tumor / genetics*
  • Biomarkers, Tumor / metabolism
  • DNA, Neoplasm / genetics
  • Female
  • Follow-Up Studies
  • Hepatectomy / mortality*
  • Humans
  • Immunoenzyme Techniques
  • Liver Neoplasms / mortality
  • Liver Neoplasms / secondary
  • Liver Neoplasms / surgery*
  • Male
  • Middle Aged
  • Mutation / genetics
  • Neoplasm Recurrence, Local / diagnosis*
  • Neoplasm Recurrence, Local / mortality
  • Neoplasm Recurrence, Local / surgery
  • Neoplasm Staging
  • Polymerase Chain Reaction
  • Prognosis
  • Retrospective Studies
  • Survival Rate
  • Tumor Suppressor Protein p53 / genetics
  • Tumor Suppressor Protein p53 / metabolism
  • Wnt Proteins / genetics
  • Wnt Proteins / metabolism
  • beta Catenin / genetics
  • beta Catenin / metabolism

Substances

  • Biomarkers, Tumor
  • CTNNB1 protein, human
  • DNA, Neoplasm
  • TP53 protein, human
  • Tumor Suppressor Protein p53
  • Wnt Proteins
  • beta Catenin