Malignant PEComa involving the mandible: report of a unique case

Jason B Untrauer; Peter J Giannini; Geoffrey A Talmon; Sonny L Johansson

doi:10.1016/j.oooo.2012.03.018

Malignant PEComa involving the mandible: report of a unique case

Oral Surg Oral Med Oral Pathol Oral Radiol. 2014 Jan;117(1):e3-8. doi: 10.1016/j.oooo.2012.03.018. Epub 2012 Aug 15.

Authors

Jason B Untrauer¹, Peter J Giannini², Geoffrey A Talmon³, Sonny L Johansson⁴

Affiliations

¹ Assistant Professor, Department of Surgery, Division of Oral and Maxillofacial Surgery, College of Medicine, University of Nebraska Medical Center, Omaha, Nebraska.
² Associate Professor, Department of Oral Biology, Section of Oral and Maxillofacial Pathology and Radiology; and Director of Clinical and Translational Research, Cruzan Center for Dental Research, College of Dentistry, University of Nebraska Medical Center, Lincoln, Nebraska. Electronic address: pgiannini@unmc.edu.
³ Assistant Professor, Department of Pathology and Microbiology, College of Medicine, University of Nebraska Medical Center, Omaha, Nebraska.
⁴ Professor and Amelia F. and Austin L. Vickery Jr. Chair of Pathology, Department of Pathology and Microbiology, College of Medicine, University of Nebraska Medical Center, Omaha, Nebraska.

PMID: 22901659
DOI: 10.1016/j.oooo.2012.03.018

Abstract

We report a unique case of a malignant perivascular epithelioid cell neoplasm (PEComa) presenting as a slow-growing mandibular lesion in a 77-year-old Caucasian female. Primary osseous involvement by PEComas is rare. This is the first reported case of a malignant PEComa arising within the jaw. The patient is currently free of disease 2 years after treatment.

Publication types

Case Reports

MeSH terms

Aged
Female
Humans
Internal Fixators
Mandibular Neoplasms / diagnostic imaging
Mandibular Neoplasms / pathology*
Mandibular Neoplasms / surgery
Mandibular Reconstruction / methods*
Perivascular Epithelioid Cell Neoplasms / diagnostic imaging
Perivascular Epithelioid Cell Neoplasms / pathology*
Perivascular Epithelioid Cell Neoplasms / surgery
Prosthesis Design / instrumentation
Prosthesis Design / methods
Tomography, X-Ray Computed