The proteasome: mechanisms of biology and markers of activity and response to treatment in multiple myeloma

Leuk Lymphoma. 2014 Aug;55(8):1707-14. doi: 10.3109/10428194.2013.828351. Epub 2014 Jan 24.

Abstract

Since the early 1990s, the synthesis and subsequent clinical application of small molecule inhibitors of the ubiquitin proteasome pathway (UPP) has revolutionized the treatment and prognosis of multiple myeloma. In this review, we summarize important aspects of the biology of the UPP with a focus on its structure and key upstream/downstream regulatory components. We then review current knowledge of plasma cell sensitivity to proteasome inhibition and highlight new proteasome inhibitors that have recently entered clinical development. Lastly, we address the putative role of circulating proteasomes as a novel biomarker in multiple myeloma and provide guidance for future clinical trials using proteasome inhibitors.

Keywords: Myeloma; cell cycle and apoptosis changes; prognostication.

Publication types

  • Review

MeSH terms

  • Animals
  • Antineoplastic Agents / therapeutic use
  • Apoptosis
  • Biomarkers
  • Humans
  • Multiple Myeloma / drug therapy
  • Multiple Myeloma / immunology
  • Multiple Myeloma / metabolism*
  • Plasma Cells / immunology
  • Plasma Cells / metabolism
  • Prognosis
  • Proteasome Endopeptidase Complex / blood
  • Proteasome Endopeptidase Complex / immunology
  • Proteasome Endopeptidase Complex / metabolism*
  • Proteasome Inhibitors / therapeutic use
  • Treatment Outcome

Substances

  • Antineoplastic Agents
  • Biomarkers
  • Proteasome Inhibitors
  • Proteasome Endopeptidase Complex