Genetic variants affecting alternative splicing of human cholesteryl ester transfer protein

Biochem Biophys Res Commun. 2014 Jan 24;443(4):1270-4. doi: 10.1016/j.bbrc.2013.12.127. Epub 2014 Jan 3.

Abstract

Cholesteryl ester transfer protein (CETP) plays an important role in reverse cholesterol transport, with decreased CETP activity increasing HDL levels. Formation of an alternative splice form lacking exon 9 (Δ9-CETP) has been associated with two single nucleotide polymorphisms (SNPs) in high linkage disequilibrium with each other, namely rs9930761 T>C located in intron 8 in a putative splicing branch site and rs5883 C>T in a possible exonic splicing enhancer (ESE) site in exon 9. To assess the relative effect of rs9930761 and rs5883 on splicing, mini-gene constructs spanning CETP exons 8 to 10, carrying all four possible allele combinations, were transfected into HEK293 and HepG2 cells. The minor T allele of rs5883 enhanced splicing significantly in both cell lines whereas the minor C allele of rs9930761 did not. In combination, the two alleles did not yield greater splicing than the rs5883 T allele alone in HepG2 cells. These results indicate that the genetic effect on CETP splicing is largely attributable to rs5883. We also confirm that Δ9-CETP protein is expressed in the liver but fails to circulate in the blood.

Keywords: Alternative splicing; CETP levels in liver and plasma; Cholesteryl ester transfer protein; Coronary artery disease; Statin.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Alleles
  • Alternative Splicing*
  • Cholesterol Ester Transfer Proteins / chemistry
  • Cholesterol Ester Transfer Proteins / genetics*
  • Cholesterol Ester Transfer Proteins / metabolism*
  • Enhancer Elements, Genetic
  • Exons
  • Genetic Variation*
  • HEK293 Cells
  • Hep G2 Cells
  • Humans
  • Introns
  • Liver / metabolism
  • Polymorphism, Single Nucleotide
  • RNA Splice Sites
  • RNA, Messenger / genetics
  • RNA, Messenger / metabolism

Substances

  • CETP protein, human
  • Cholesterol Ester Transfer Proteins
  • RNA Splice Sites
  • RNA, Messenger