Abstract
Remnants of the right valve of the sinus venosus, which fail to regress may present as an obstructing membrane within the right atrium as a very rare congenital anomaly. When associated with an atrial septal defect, primary cyanosis may occur due to a large right-to-left shunt. We report on a 1-week old girl with a pseudo-cor triatriatum dexter and immediate cyanosis after an uncomplicated birth. She was successfully treated with surgical excision of the obstructing membrane.
Keywords:
Cardiac surgery; Congenital; Cor triatriatum; Cyanosis; Right atrium.
Publication types
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Case Reports
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Video-Audio Media
MeSH terms
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Cardiac Surgical Procedures
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Cor Triatriatum / complications*
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Cor Triatriatum / diagnosis
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Cor Triatriatum / physiopathology
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Cor Triatriatum / surgery
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Cyanosis / diagnosis
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Cyanosis / etiology*
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Cyanosis / physiopathology
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Echocardiography, Doppler, Color
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Female
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Heart Septal Defects, Atrial / complications*
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Heart Septal Defects, Atrial / diagnosis
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Heart Septal Defects, Atrial / physiopathology
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Heart Septal Defects, Atrial / surgery
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Humans
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Infant, Newborn
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Treatment Outcome
Supplementary concepts
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Atrial Septal Defect Sinus Venosus