Mucinous borderline tumours of the ovary and the appendix: a retrospective study and overview of the literature

Gynecol Oncol. 2014 May;133(2):155-8. doi: 10.1016/j.ygyno.2014.02.013. Epub 2014 Feb 16.

Abstract

Objectives: Appendectomy is often recommended in patients with mucinous borderline ovarian tumours (mBOTs) based on studies suggesting that metastatic disease from a primary appendiceal tumour can mimic mBOT. The present study assessed the incidence of mucinous neoplasms in the appendix associated with the presence of mBOT.

Methods: A retrospective cohort study was performed in two university hospitals in the Netherlands between 1990 and 2011. All patients with mBOT and/or a mucinous appendiceal tumour were included.

Results: Of 127 patients included, 98 had a primary mBOT and 29 had a primary mucinous appendiceal tumour. In patients with a mBOT, the appendix was either removed at prior surgery (4%), resected as part of the staging procedure showing no pathological abnormalities (13%), described as normal and not resected (58%), or not described and not resected (25%). During a median follow-up period of 5 years (range 2-23), two patients developed a recurrence in which the appendix was not involved. In all patients with a primary mucinous tumour of the appendix, the appendix appeared abnormal at the time of surgery. Eight of these patients (28%) were diagnosed with invasive ovarian metastases. A review of the literature including the cases from this study identified 510 mucinous ovarian tumours with borderline features and 214 associated appendectomies, of which 4 (1.9%) contained a primary appendiceal malignancy.

Conclusions: A thorough inspection of the appendix should be performed in patients with a mucinous ovarian tumour with borderline features. An appendectomy should only be performed when the appendix is macroscopically abnormal.

Keywords: Appendix; Borderline tumour of the ovary.

Publication types

  • Review

MeSH terms

  • Adenocarcinoma, Mucinous / secondary*
  • Adenocarcinoma, Mucinous / surgery
  • Appendectomy
  • Appendiceal Neoplasms / pathology*
  • Appendiceal Neoplasms / surgery
  • Cohort Studies
  • Diagnosis, Differential
  • Female
  • Humans
  • Netherlands
  • Ovarian Neoplasms / secondary*
  • Ovarian Neoplasms / surgery
  • Ovariectomy
  • Retrospective Studies