The role of infections in Behçet disease and neuro-Behçet syndrome

Autoimmun Rev. 2015 Jul;14(7):609-15. doi: 10.1016/j.autrev.2015.02.009. Epub 2015 Mar 11.

Abstract

Infections are considered an environmental trigger for exacerbations of immune-mediated diseases. We aimed to establish if common viral infections could be identified as a precipitant of Behçet disease (BD) with or without neurological involvement and to assess the variability of the immune response to common viruses. We also investigated whether cytokines and chemokines could be markers of neurological involvement. Finally, we explored if anti-basal ganglia antibodies (ABGAs) would be associated with neurological involvement in BD. Our study included 14 individuals with BD with neurological involvement (neuroBehçet syndrome - NBS), 16 individuals with BD without neurological involvement and 18 healthy controls (HC). Overall we found a tendency for increased levels of anti-viral IgG antibody levels in BD, more evident in NBS patients versus HC. Epstein-Barr viral-capsid antigen IgG titres were increased in NBS patients versus other BD patients (p=0.032). Anti-measles antibody titres induced by vaccination were similarly elevated. ABGAs were not detected in the serum of our cohort. Raised levels of serum IL-8 in some BD patients did not reflect clinical activity or severity. In conclusion, there was evidence for a polyclonal immune activation rather than a specific virus effect in the sera of individuals with BD or NBS.

Keywords: Behçet; EBV; IL-8; Infections.

Publication types

  • Review

MeSH terms

  • Antibodies, Viral / immunology
  • Antigens, Viral / immunology
  • Behcet Syndrome / complications
  • Behcet Syndrome / immunology*
  • Behcet Syndrome / virology
  • Capsid Proteins / immunology
  • Central Nervous System Diseases / complications
  • Central Nervous System Diseases / immunology*
  • Central Nervous System Diseases / virology
  • Humans
  • Immunoglobulin G / immunology
  • Virus Diseases / complications
  • Virus Diseases / immunology*

Substances

  • Antibodies, Viral
  • Antigens, Viral
  • Capsid Proteins
  • Epstein-Barr viral capsid antigen
  • Immunoglobulin G