High-throughput somatic mutation profiling in pulmonary sarcomatoid carcinomas using the LungCarta™ Panel: exploring therapeutic targets

Ann Oncol. 2015 Aug;26(8):1748-53. doi: 10.1093/annonc/mdv232. Epub 2015 May 12.

Abstract

Background: Pulmonary sarcomatoid carcinomas (SC) are tumors characterized by poor prognosis and resistance to conventional platinum-based chemotherapy. This study sought to describe the mutational profile of SC using high-throughput genotyping technology.

Patients and methods: We used mass spectrometry to test 114 surgical biopsies from 81 patients with SC for 214 mutations affecting 26 oncogenes and tumor suppressor genes.

Results: In total, 75 (92.6%) patients were smokers. Within the total 81 tumors, 67 distinct somatic alterations were identified, with 56 tumors (69.1%) harboring at least one mutation. The most frequent mutations were KRAS (27.2%), EGFR (22.2%), TP53 (22.2%), STK11 (7.4%), NOTCH1 (4.9%), NRAS (4.9%), and PI3KCA (4.9%). The EGFR mutations were almost always rare mutations (89%). In 32 tumors (39.5%), two or more mutations co-existed, with up to four mutations in a single case. In six different cases, comparative genetic analysis of different histological areas from the same tumor (giant, spindle, or epithelial component) revealed a 61% concordance rate for all the mutations with a 10% detection threshold, compared with 91.7% with a 20% detection threshold.

Conclusion: Our results demonstrated a high mutation rate and frequent co-mutations. Despite SC tumors exhibiting a high histological heterogeneity, some intratumoral molecular homogeneity was found. Now with newly developed targeted therapies, SC patients may be eligible for new target mutations, and can now therefore be screened for clinical trials.

Keywords: EGFR; KRAS; lung sarcomatoid carcinoma; mutation; nonsmall-cell lung cancer.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • AMP-Activated Protein Kinase Kinases
  • Adult
  • Aged
  • Carcinoma / genetics
  • Carcinoma, Giant Cell / genetics*
  • Carcinoma, Non-Small-Cell Lung / genetics*
  • Carcinosarcoma / genetics*
  • Cohort Studies
  • ErbB Receptors / genetics
  • Female
  • GTP Phosphohydrolases / genetics
  • High-Throughput Nucleotide Sequencing
  • Humans
  • Lung Neoplasms / genetics*
  • Male
  • Membrane Proteins / genetics
  • Middle Aged
  • Mutation
  • Nuclear Proteins / genetics
  • Protein Serine-Threonine Kinases / genetics
  • Proto-Oncogene Proteins p21(ras) / genetics
  • Receptor, Notch1 / genetics
  • Retrospective Studies
  • Transcription Factors / genetics
  • Tumor Suppressor Protein p53 / genetics

Substances

  • KRAS protein, human
  • Membrane Proteins
  • NOTCH1 protein, human
  • Nuclear Proteins
  • PI3KCA protein, human
  • Receptor, Notch1
  • TP53 protein, human
  • Transcription Factors
  • Tumor Suppressor Protein p53
  • EGFR protein, human
  • ErbB Receptors
  • Protein Serine-Threonine Kinases
  • STK11 protein, human
  • AMP-Activated Protein Kinase Kinases
  • GTP Phosphohydrolases
  • NRAS protein, human
  • Proto-Oncogene Proteins p21(ras)