Health Related Quality of Life in Indian Children with Cystic Fibrosis

Indian Pediatr. 2015 May;52(5):403-8. doi: 10.1007/s13312-015-0645-7.

Abstract

Objective: This study was devised to translate Cystic Fibrosis Questionnaire-Revised to Hindi and administer it to Indian children and adolescents diagnosed with cystic fibrosis.

Design: Cross-sectional study.

Setting: This study was carried out in cystic fibrosis patients attending Pediatric Chest Clinic of a tertiary-care hospital in Northern India from July 2012 to December 2012.

Participants: 45 children (6-13 years) and their parents, and 14 adolescents. Patients with unstable health in the past two weeks were excluded.

Intervention: Cystic Fibrosis Questionnaire- Revised translated in Hindi was administered. Clinical evaluation and scoring, throat swab cultures and spirometry were also done during the same visit.

Main outcome measures: Health Related Quality of Life scores were the primary measures, and clinical scores, swab cultures and spirometry were secondary measures.

Results: Cronbachs alpha ranged from 0.020-0.863.The Factor analysis indicated that most test-items correlated more with competing scales than the intended scales. Convergence between self and proxy-rating was found to be dependent on the domain. The Cystic Fibrosis Questionnaire- Revised scores correlated well with clinical scores (r=0.65,P=0.011), Pseudomonas spp culture data and pulmonary function tests. There was an inverse relation between Health Related Quality of Life scores and age at diagnosis (r=-0.339, P=0.02).

Conclusions: Hindi versions of Cystic Fibrosis Questionnaire- Revised: Child, Adolescent and Parents instruments will act as an important step towards data on Health Related Quality of Life of Indian patients with cystic fibrosis.

MeSH terms

  • Adolescent
  • Child
  • Cross-Sectional Studies
  • Cystic Fibrosis / epidemiology*
  • Cystic Fibrosis / physiopathology*
  • Female
  • Humans
  • India / epidemiology
  • Male
  • Quality of Life*
  • Severity of Illness Index
  • Spirometry
  • Surveys and Questionnaires
  • Treatment Outcome