A case of concomitant intralobar bronchopulmonary sequestration and situs inversus totalis

Clin Respir J. 2017 May;11(3):391-393. doi: 10.1111/crj.12345. Epub 2015 Aug 3.

Abstract

Background and aims: Situs inversus is a rare congenital abnormality involving partial or complete transposition of the thoracic or abdominal viscera. In situs inversus totalis, both the thoracic and abdominal viscera are transposed. The incidence of this condition is 0.01% to 0.02%. Bronchopulmonary sequestration (BPS) is a rare congenital abnormality of the respiratory tract with an incidence of 0.15% to 1.80%. Intralobar sequestration is uncommonly associated with congenital anomalies.

Methods: A routine chest X-ray of a 41-year-old asymptomatic man showed dextrocardia, a left-sided liver, right-sided stomach, and left paracardiac opacity.

Results: Computed tomography (CT) and CT pulmonary angiography revealed dextrocardia with situs inversus totalis and left paracardiac intralobar BPS in the lingular segment of the left upper lobe.

Conclusion: We present a rare case of combined situs inversus totalis and intralobar BPS with an atypical location and feeder artery.

Keywords: bronchopulmonary - sequestrationcomputed tomography - situs inversus totalis.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Bronchopulmonary Sequestration / complications*
  • Bronchopulmonary Sequestration / diagnostic imaging
  • Bronchopulmonary Sequestration / epidemiology
  • Computed Tomography Angiography / methods
  • Congenital Abnormalities / pathology
  • Dextrocardia / diagnostic imaging*
  • Hospitalization
  • Humans
  • Incidence
  • Lung / abnormalities*
  • Lung / blood supply
  • Lung / diagnostic imaging*
  • Male
  • Pneumonia / complications
  • Radiography, Thoracic / methods
  • Rare Diseases
  • Respiratory System Abnormalities / complications*
  • Respiratory System Abnormalities / diagnostic imaging
  • Respiratory System Abnormalities / epidemiology
  • Situs Inversus / complications*
  • Situs Inversus / diagnostic imaging
  • Situs Inversus / epidemiology
  • Tomography, X-Ray Computed / methods