Bilateral encephaloduroarteriosynangiosis (EDAS) in a 6-year-old female for moyamoya disease: case report and technical note with 12-year follow-up

Childs Nerv Syst. 2016 Apr;32(4):745-7. doi: 10.1007/s00381-015-2876-2. Epub 2015 Aug 19.

Abstract

Purpose: To demonstrate that despite disease progression, indirect cerebral revascularisation via EDAS for moyamoya disease is able to maintain sufficient collateral blood supply over a 12-year period.

Methods: Case report of an individual patient with surgically managed moyamoya disease followed up with imaging and outpatient clinic assessments.

Results: Follow-up imaging and assessment over 12 years concluded with a good functional and radiographic outcome.

Conclusion: The extensive follow-up in our case of a 6-year-old female treated with bilateral EDAS procedures for moyamoya disease demonstrates that despite disease progression over 12 years, sufficient collateral blood supply was maintained to achieve a good functional outcome.

Keywords: Cerebral revascularisation; EDAS; Encephaloduroarteriosynangiosis; Moyamoya disease.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Angiography, Digital Subtraction
  • Cerebral Angiography
  • Cerebral Revascularization / methods*
  • Female
  • Humans
  • Longitudinal Studies
  • Moyamoya Disease / diagnostic imaging
  • Moyamoya Disease / surgery*