Post-translational control of RIPK3 and MLKL mediated necroptotic cell death

F1000Res. 2015 Nov 19:4:F1000 Faculty Rev-1297. doi: 10.12688/f1000research.7046.1. eCollection 2015.

Abstract

Several programmed lytic and necrotic-like cell death mechanisms have now been uncovered, including the recently described receptor interacting protein kinase-3 (RIPK3)-mixed lineage kinase domain-like (MLKL)-dependent necroptosis pathway. Genetic experiments have shown that programmed necrosis, including necroptosis, can play a pivotal role in regulating host-resistance against microbial infections. Alternatively, excess or unwarranted necroptosis may be pathological in autoimmune and autoinflammatory diseases. This review highlights the recent advances in our understanding of the post-translational control of RIPK3-MLKL necroptotic signaling. We discuss the critical function of phosphorylation in the execution of necroptosis, and highlight the emerging regulatory roles for several ubiquitin ligases and deubiquitinating enzymes. Finally, based on current evidence, we discuss the potential mechanisms by which the essential, and possibly terminal, necroptotic effector, MLKL, triggers the disruption of cellular membranes to cause cell lysis.

Keywords: MLKL; RIPK3; mixed lineage kinase domain-like; necroptosis; necroptotic cell death; receptor interacting protein kinase-3.

Publication types

  • Review

Grants and funding

The authors are grateful to the National Health and Medical Research Council of Australia for support via a fellowship to JEV (1052598), project grants (1057905, 1067289, 1051210) and the IRIISS scheme (9000220), and the Australian Research Council for fellowship support to JMM (FT100100100). Additional support was provided by Victorian State Government Operational Infrastructure Support Scheme.