Orphan proteins of unknown function in the mitochondrial intermembrane space proteome: New pathways and metabolic cross-talk

Biochim Biophys Acta. 2016 Nov;1863(11):2613-2623. doi: 10.1016/j.bbamcr.2016.07.004. Epub 2016 Jul 15.

Abstract

The mitochondrial intermembrane space (IMS) is involved in protein transport, lipid homeostasis and metal ion exchange, while further acting in signalling pathways such as apoptosis. Regulation of these processes involves protein modifications, as well as stress-induced import or release of proteins and other signalling molecules. Even though the IMS is the smallest sub-compartment of mitochondria, its redox state seems to be tightly regulated. However, the way in which this compartment participates in the cross-talk between the multiple organelles and the cytosol is far from understood. Here we focus on newly identified IMS proteins that may represent future challenges in mitochondrial research. We present an overview of the import pathways, the recently discovered new components of the IMS proteome and how these relate to key aspects of cell signalling and progress made in stem cell and cancer research.

Keywords: Intermembrane space; Metabolism; Mitochondria; Mitochondrial proteome; Protein import; Redox signalling.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Alzheimer Disease / metabolism
  • Alzheimer Disease / pathology
  • Animals
  • Apoptosis
  • Biological Transport
  • Calcium Signaling
  • Energy Metabolism*
  • Epigenesis, Genetic
  • Humans
  • Mitochondria / metabolism*
  • Mitochondria / pathology
  • Mitochondrial Membranes / metabolism*
  • Mitochondrial Membranes / pathology
  • Mitochondrial Proteins / genetics
  • Mitochondrial Proteins / metabolism*
  • Proteome*
  • Signal Transduction*

Substances

  • Mitochondrial Proteins
  • Proteome