Paraneoplastic pemphigus (PNP) is an autoimmune blistering disease associated with neoplasms. The disease is most commonly of lymphoproliferative origin and presents high mortality. We describe a patient with PNP and myasthenia gravis associated with inflammatory pseudotumor-like follicular dendritic cell sarcoma, as well as the response to rituximab.
Keywords: Inflammatory pseudotumor‐like follicular dendritic cell sarcoma; myasthenia gravis; paraneoplastic pemphigus; rituximab.