Novel GNB1 missense mutation in a patient with generalized dystonia, hypotonia, and intellectual disability

Neurol Genet. 2016 Sep 13;2(5):e106. doi: 10.1212/NXG.0000000000000106. eCollection 2016 Oct.

Abstract

Recently, exome sequencing has extended our knowledge of genetic causes of developmental delay through identification of de novo, germline mutations in the guanine nucleotide-binding protein, beta 1 (GNB1) in 13 patients with neurodevelopmental disability and a wide range of additional symptoms and signs including hypotonia in 11 and seizures in 10 of the patients. Limb/arm dystonia was found in 2 patients.(1).