Soluble adenylyl cyclase is essential for proper lysosomal acidification

J Gen Physiol. 2016 Oct;148(4):325-39. doi: 10.1085/jgp.201611606.

Abstract

Lysosomes, the degradative organelles of the endocytic and autophagic pathways, function at an acidic pH. Lysosomes are acidified by the proton-pumping vacuolar ATPase (V-ATPase), but the molecular processes that set the organelle's pH are not completely understood. In particular, pH-sensitive signaling enzymes that can regulate lysosomal acidification in steady-state physiological conditions have yet to be identified. Soluble adenylyl cyclase (sAC) is a widely expressed source of cAMP that serves as a physiological pH sensor in cells. For example, in proton-secreting epithelial cells, sAC is responsible for pH-dependent translocation of V-ATPase to the luminal surface. Here we show genetically and pharmacologically that sAC is also essential for lysosomal acidification. In the absence of sAC, V-ATPase does not properly localize to lysosomes, lysosomes fail to fully acidify, lysosomal degradative capacity is diminished, and autophagolysosomes accumulate.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Adenylyl Cyclases / genetics
  • Adenylyl Cyclases / metabolism*
  • Animals
  • Brain / metabolism
  • Brain / ultrastructure
  • Cell Line
  • Fibroblasts / metabolism*
  • Gene Expression Regulation, Enzymologic
  • Lysosomes
  • Mice
  • Mice, Knockout
  • Purines

Substances

  • PH006 compound
  • Purines
  • Adenylyl Cyclases