A 10-year old girl with generalized benign atrophic epidermolysis bullosa (EB) developed large nevomelanocytic nevi over a period of 1 year. Since such nevoid lesions have been repeatedly observed in other patients with generalized benign atrophic EB they should be regarded as a characteristic clinical feature of this type of mechanobullous disease. Regular observation of such patients will demonstrate the significance of these pigmented lesions as precursors of malignant melanoma.