Case report-malignant transformation in Cronkhite-Canada syndrome polyp

Medicine (Baltimore). 2017 Feb;96(6):e6051. doi: 10.1097/MD.0000000000006051.

Abstract

Rationale: Cronkhite-Canada syndrome (CCS) is a rare disease, the etiology of CCS is currently unknown. Although CCS is widely accepted as a benign disorder, the malignant potential of the polyps in CCS patients is yet controversial.

Patient concerns: A 55-year-old Chinese male was first admitted to Beijing Friendship Hospital with a 3-month history of frequent watery diarrhea (10-15 times/day), loss of taste, and a weight loss of 10 kg in August 2010. The left heel bone fracture in the patient occurred about 2 weeks prior to his diarrhea.

Diagnoses: He was diagnosed as Cronkhite-Canada syndrome.

Interventions: Oral administration of prednisone was initiated at a dosage of 20 mg/day.

Outcomes: After 3 months of treatment, the clinical manifestations disappeared, and colonoscopy showed sparsely distributed small polyps in the colon. Consequently, the dose of prednisone was reduced to 10mg. However, after 4 months, his fingernails were again found atrophic along with mild abdominal discomfort without diarrhea. Colonoscopy revealed a recurrence of the polyps in March 2011. The treatment was repeated with prednisone at a dosage of 20 mg/day resulting in subsided symptoms. In September 2011, he underwent colonoscopy although no significant clinical manifestations were observed. In addition, the polyp in the sigmoid colon was cancerated.

Lessons: The present case indicated that the physical stress was related to CCS and malignant transformation occurred in Cronkhite-Canada syndrome polyp. After the diffused inflammatory polyps have responded to steroid therapy, other existing adenomas require endoscopic treatments, which can decrease the possibility of neoplastic transformation.

Publication types

  • Case Reports

MeSH terms

  • Cell Transformation, Neoplastic / pathology*
  • Colonic Polyps / pathology*
  • Humans
  • Intestinal Polyposis / diagnosis
  • Intestinal Polyposis / drug therapy
  • Intestinal Polyposis / pathology*
  • Male
  • Middle Aged
  • Prednisone / therapeutic use

Substances

  • Prednisone