Nutrition: Prevention and management of nutritional failure in Cystic Fibrosis

Jillian S Sullivan; Maria R Mascarenhas

doi:10.1016/j.jcf.2017.07.010

Nutrition: Prevention and management of nutritional failure in Cystic Fibrosis

J Cyst Fibros. 2017 Nov:16 Suppl 2:S87-S93. doi: 10.1016/j.jcf.2017.07.010.

Authors

Jillian S Sullivan¹, Maria R Mascarenhas²

Affiliations

¹ Department of Pediatrics, University of Vermont Children's Hospital, Burlington, VT, USA. Electronic address: Jillian.sullivan@uvmhealth.org.
² Department of Pediatrics, Children's Hospital of Philadelphia, Philadelphia, PA, USA. Electronic address: mascarenhas@email.chop.edu.

PMID: 28986026
DOI: 10.1016/j.jcf.2017.07.010

Abstract

Close monitoring of nutritional status is critical to the overall health of a patient with CF. As part of routine CF care, measurement of weight and height (and calculation of weight/length or BMI as appropriate) should be performed and analyzed at each visit. Early recognition of nutritional risk is imperative and evaluation with a multidisciplinary team should be performed to assess for caloric intake, caloric malabsorption, and other causes of poor weight gain and growth. Many tools are available to use for intervention, including oral supplementation, behavioral interventions, medications, nutritional therapies, and enteral tube feeding.

Keywords: Cystic fibrosis; Enteral feeding; Fat soluble vitamins; Nutrition.

Publication types

Review

MeSH terms

Cystic Fibrosis / complications*
Humans
Malnutrition* / diagnosis
Malnutrition* / etiology
Malnutrition* / physiopathology
Malnutrition* / prevention & control
Nutritional Status
Patient Care Management / methods*