Background: Nuclear protein of the testis (NUT) midline carcinoma is genetically defined by rearrangement of NUT or by immunohistochemical expression of NUT.
Findings: A 6-year old child had a NUT midline carcinoma of the lung. Despite aggressive therapy, the child died.
Conclusion: NUT carcinoma, which can be diagnosed immunohistochemically, remains an aggressive tumor.
Keywords: NUT midline carcinoma; immünohistochemistry; pulmonary.