Clinicopathological features of combined hepatocellular-cholangiocarcinoma with sarcomatous change: Case report and literature review

Medicine (Baltimore). 2018 Jan;97(3):e9640. doi: 10.1097/MD.0000000000009640.

Abstract

Rationale: Combined hepatocellular-cholangiocarcinoma (cHCC-CC) is a rare subtype of primary liver malignancy comprising <1.5% of all primary liver tumors. Sarcomatoid changes in cHCC-CC are even rarer. Due to the rarity of this subtype, its clinicopathological feature is poorly understood. Therefore, here we report 2 tumors.

Patient concerns: The first patient was a 44-year-old man with 5-year history of hepatitis B-induced cirrhosis. The resection of right liver revealed a 2.5 × 2.5 × 2 cm tumor mass. Histologically, the tumor showed areas of the typical moderately differentiated HCC. An intermingled adenocarcinoma with pleomorphic and spindle-shaped cells was also identified. The second case involved a 54-year-old man with a history of hepatitis B-induced cirrhosis. A 3.5 × 3 × 3 cm mass was found in the middle left of falciform ligament. Microscopically, the tumor consisted of spindle-shaped sarcomatoid carcinoma cells mixed with typical well-differentiated HCC and well-differentiated CC.

Diagnoses: According to the clinicopathological features, diagnosis of cHCC-CC with sarcomatous change was made.

Interventions: In the first case, right lobectomy of the liver was performed. The second patient underwent laparoscopic, hepatic left lateral lobectomy.

Outcomes: The first patient was alive and well 10 years after the surgical resection without additional treatment. In second case, at 8 months after surgical resection, there was no evidence of recurrence or metastasis.

Lessons: In this report, we describe 2 rare cases of cHCC-CC with sarcomatous change, and findings are helpful for the pathologists would like to further identify the clinicopathological features of this rare tumor.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Bile Duct Neoplasms / pathology*
  • Carcinoma, Hepatocellular / pathology*
  • Cholangiocarcinoma / pathology*
  • Humans
  • Liver Neoplasms / pathology*
  • Male
  • Middle Aged
  • Neoplasms, Multiple Primary / pathology*