[Pigmented dermatofibrosarcoma protuberans (Bednar's tumor)]

Med Cutan Ibero Lat Am. 1988;16(4):314-8.
[Article in Spanish]

Abstract

Pigmented dermatofibrosarcoma protuberans, first described by Bednar under the term storiform neurofibroma, is an infrequent neoplasm accounting for 1 to 5% of cases of dermatofibrosarcoma protuberans. Bednar's tumor is composed of spindle shaped cells arranged in a distinctive storiform or carthwheel pattern, and melanin-containing dendritic cells scattered within the tumor. The differential diagnosis with (non-pigmented) dermatofibrosarcoma protuberans is based on the presence of this population of pigmented cells. Two cases of pigmented dermatofibrosarcoma protuberans (Bednar's tumor) are reported here in, and a discussion follows on the clinicopathological features of this neoplasm and the different hypotheses on its histogenesis.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Child
  • Female
  • Fibrosarcoma / pathology*
  • Fibrosarcoma / ultrastructure
  • Humans
  • Male
  • Skin Neoplasms / pathology*
  • Skin Neoplasms / ultrastructure