Constrictive pericarditis in a patient with inherited factor VII deficiency

Ter Arkh. 2018 Aug 17;90(7):86-90. doi: 10.26442/terarkh201890786-90.

Abstract

Constrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient with rare inherited bleeding disorder - factor VII deficiency. Heart failure due to CP was suspected based on clinical symptoms, results of ultrasonic and radiological investigations. The diagnosis was verified by the results of cardiac magnetic resonance imaging. Pericardectomy was performed resulting in significant improvement in the patient's condition.

Keywords: VII factor deficiency; constrictive pericarditis; hypoproconvertinemia; pericardectomy.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Electrocardiography
  • Factor VII Deficiency / complications
  • Factor VII Deficiency / diagnosis
  • Factor VII Deficiency / surgery*
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Pericardiectomy*
  • Pericarditis, Constrictive / complications
  • Pericarditis, Constrictive / diagnostic imaging
  • Pericarditis, Constrictive / surgery*
  • Tomography, X-Ray Computed
  • Treatment Outcome