Multifocal lymphangioendotheliomatosis without thrombocytopenia or clinical signs of systemic bleeding

Pediatr Dermatol. 2019 Nov;36(6):965-966. doi: 10.1111/pde.13959. Epub 2019 Aug 25.

Abstract

Multifocal lymphangioendotheliomatosis with thrombocytopenia (MLT) is an extremely rare recently described disorder characterized by diffuse congenital skin and gastrointestinal vascular lesions that may be associated with gastrointestinal bleeding and thrombocytopenia. We herein present a case report of multifocal lymphangioendotheliomatosis without thrombocytopenia or extensive extracutaneous involvement (gastrointestinal bleeding). Given the high morbidity and mortality associated with this disease, it is important for clinicians to recognize this disorder in order to select the most appropriate therapeutic approach.

Keywords: neonatal; vascular malformation.

Publication types

  • Case Reports

MeSH terms

  • Female
  • Humans
  • Infant
  • Lymphangioma / congenital
  • Lymphangioma / pathology*
  • Skin Neoplasms / congenital
  • Skin Neoplasms / pathology*
  • Twins, Monozygotic