Strategy for molecular cloning of the fragile X site DNA

Am J Med Genet. 1988 May-Jun;30(1-2):613-23. doi: 10.1002/ajmg.1320300162.

Abstract

Fragile X syndrome is a common form of mental retardation associated with a fragile site on the human X chromosome. We have recently demonstrated that the fragile X chromosome, when isolated within a somatic cell hybrid, often participates in translocations involving rodent chromosome arms. Cytogenetic and molecular evidence strongly suggests that the human breakpoint of these translocations is within the fragile X sequence. Hence, the joining of heterologous DNA (i.e. from two species) may permit the molecular cloning of the fragile X site. We describe here the cloning approach employed to enhance the isolation of interspecific chromosome translocation junctions. The human portion of the translocation junction should be derived from the fragile X site sequence.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Cloning, Molecular*
  • Cosmids
  • DNA, Recombinant*
  • Fragile X Syndrome / genetics*
  • Humans
  • Hybrid Cells
  • Sex Chromosome Aberrations / genetics*
  • Translocation, Genetic
  • X Chromosome*

Substances

  • DNA, Recombinant