Ovarian tumors in children: how common are lesion recurrence and metachronous disease? A UK CCLG Surgeons Cancer Group nationwide study

J Pediatr Surg. 2020 Oct;55(10):2026-2029. doi: 10.1016/j.jpedsurg.2019.10.059. Epub 2019 Nov 26.

Abstract

Background: Ovarian tumors in children are rare, mature teratoma being the most common histological entity. Robust guidelines to aid patient follow-up after resection are distinctly lacking. Although mature teratoma has a very good prognosis following complete resection, small studies have reported the occurrence of metachronous disease and recurrence to a variable degree (2.5-23% of patients). Nevertheless, there are surgeons who recommend no follow-up is required for these children after primary tumor resection. We investigated the incidence of (i) recurrence and (ii) metachronous disease in pediatric patients following ovarian tumor resection.

Methods: Retrospective multicenter study amongst UK pediatric surgical oncology centers. Females <16 years with diagnosis of ovarian tumor from 2006 to 2016 were included. Functional/neonatal ovarian cysts were excluded.

Results: Three hundred ten patients with ovarian tumors treated at 12 surgical oncology centers were identified. Mean age at surgery was 11 years [IQR 8-14]. Most common diagnosis were mature teratoma (57%, 177 cases), immature teratoma (10.9%, 34 cases) and serous cystadenoma (7.7%, 24 cases). 8.1% (25 cases) of all females were identified with tumor recurrence/ metachronous disease. 5.1% (9 cases) of patients with mature teratoma had recurrent/ metachronous disease. Most of these patients were diagnosed at routine clinic follow-up.

Conclusion: Our study clearly shows that ovarian tumor recurrence(s) and metachronous disease occur, even in "benign" ovarian tumors. We recommend female pediatric patients should have robust follow-up care plans after primary diagnosis and resection of ovarian tumor(s).

Level of evidence statement: This is a level II evidence study. It is a retrospective multicentre collaborative study which summarizes data from a national cohort of children.

Keywords: Adolescent; Follow-up; Ovarian teratoma; Ovarian tumor; Ovary-sparing surgery; Pediatric; UK CCLG Surgeons.

MeSH terms

  • Adolescent
  • Child
  • Female
  • Humans
  • Neoplasm Recurrence, Local* / epidemiology
  • Neoplasm Recurrence, Local* / pathology
  • Ovarian Neoplasms* / epidemiology
  • Ovarian Neoplasms* / pathology
  • Retrospective Studies
  • Teratoma* / epidemiology
  • Teratoma* / pathology
  • United Kingdom