Knocking 'em Dead: Pore-Forming Proteins in Immune Defense

Annu Rev Immunol. 2020 Apr 26:38:455-485. doi: 10.1146/annurev-immunol-111319-023800. Epub 2020 Jan 31.

Abstract

Immune cells use a variety of membrane-disrupting proteins [complement, perforin, perforin-2, granulysin, gasdermins, mixed lineage kinase domain-like pseudokinase (MLKL)] to induce different kinds of death of microbes and host cells, some of which cause inflammation. After activation by proteolytic cleavage or phosphorylation, these proteins oligomerize, bind to membrane lipids, and disrupt membrane integrity. These membrane disruptors play a critical role in both innate and adaptive immunity. Here we review our current knowledge of the functions, specificity, activation, and regulation of membrane-disrupting immune proteins and what is known about the mechanisms behind membrane damage, the structure of the pores they form, how the cells expressing these lethal proteins are protected, and how cells targeted for destruction can sometimes escape death by repairing membrane damage.

Keywords: MLKL; apoptosis; complement; cytotoxic lymphocyte; gasdermin; granulysin; microptosis; necroptosis; necrosis; perforin; pyroptosis.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Animals
  • Apoptosis / genetics
  • Apoptosis / immunology
  • Biomarkers
  • Cell Membrane / immunology
  • Cell Membrane / metabolism
  • Complement Membrane Attack Complex
  • Complement System Proteins / immunology
  • Complement System Proteins / metabolism
  • Cytotoxicity, Immunologic*
  • Gene Expression Regulation
  • Host-Pathogen Interactions / immunology*
  • Humans
  • Immune System / immunology
  • Immune System / metabolism
  • Immunity*
  • Lipid Metabolism
  • Necroptosis / genetics
  • Necroptosis / immunology
  • Necrosis / genetics
  • Necrosis / immunology
  • Necrosis / metabolism
  • Pore Forming Cytotoxic Proteins / chemistry
  • Pore Forming Cytotoxic Proteins / genetics
  • Pore Forming Cytotoxic Proteins / metabolism*
  • Structure-Activity Relationship

Substances

  • Biomarkers
  • Complement Membrane Attack Complex
  • Pore Forming Cytotoxic Proteins
  • Complement System Proteins