Hemolytic anemia and susceptibility to hydrogen-peroxide hemolysis in children with vitamin E-deficiency and chronic liver disease

J Med. 1988;19(5-6):317-34.

Abstract

Thirty-four children, aged 1-14 years, with severe chronic liver disease were studied to determine the incidence of chronic hemolytic anemia and the mechanism underlying it. Sixteen children were grouped as vitamin E-deficient patients (Group I, serum vitamin E level below 5.0 micrograms/ml) and compared with 18 vitamin E-sufficient children (Group II) and 20 healthy controls. Group I patients had a significantly lower hemoglobin level (11.6 +/- 0.4 g/dl) when compared with Group II (12.9 +/- 0.4 g/dl, less than 0.05), their RBC's were less resistant to H2O2-induced hemolysis (53.1 +/- 8.0% in Group I, vs. 1.07 +/- 0.23% in Group II), and the average hemolysis correlated with serum vitamin E levels. H2O2-induced hemolysis reverted to normal in five patients after vitamin E therapy. With respect to controls, cirrhotic children in both groups showed a slight increase in total RBC membrane lipids, but no difference in either phospholipid content or in cholesterol/phospholipid molar ratio that could have changed RBC membrane properties and sensitivity to lysis. In our experience, vitamin E-deficient cirrhotics have a slight degree of chronic hemolytic anemia and their RBC's are much more sensitive to H2O2 lysis, although this abnormal lysis susceptibility does not seem apparently related to membrane peroxidation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Anemia, Hemolytic / blood
  • Anemia, Hemolytic / complications*
  • Child
  • Child, Preschool
  • Chronic Disease
  • Disease Susceptibility
  • Erythrocyte Membrane / metabolism
  • Hemolysis / drug effects*
  • Humans
  • Hydrogen Peroxide / pharmacology*
  • Infant
  • Lipid Metabolism
  • Lipids / blood
  • Liver Diseases / blood
  • Liver Diseases / complications*
  • Liver Diseases / physiopathology
  • Liver Function Tests
  • Oxidation-Reduction
  • Vitamin E Deficiency / blood
  • Vitamin E Deficiency / complications*
  • Vitamin E Deficiency / physiopathology

Substances

  • Lipids
  • Hydrogen Peroxide